Searchable abstracts of presentations at key conferences in endocrinology

ea0085p51 | Adrenal 2 | BSPED2022

Paediatric adrenocortical carcinoma presents with virilization and glucocorticoid deficiency – a rare presentation

Dimarsha de Silva U. A .M. , Suntharesan Jananie , Somathilaka Mahendra , Liyanage Janath , A. Hemali de Silva M.

Background: Adrenocortical carcinoma in childhood is a rare tumour which accounts for about 0.2% of all paediatric malignancies. Affected children usually present with virilization, cushingoid features, and/or mineralocorticoid excess. We present a boy with adrenal carcinoma presented with virilization and unusually suppressed cortisol at initial presentation.Case report: A two-year-old boy presented with pubic hair, acne, and increased penile growth wit...